Advanced Biomedical Research

Hallervorden-Spatz disease

Authors

Department of Neurology, Shahid Sadooghi Hospital, Isfahan, Iran

Abstract

Hallervorden-Spatz disease (HSD) is a rare disorder characterized by progressive extrapyramidal dysfunction and dementia. Hallervorden and Spatz first described the disease, in 1922 as a form of familial brain degeneration characterized by iron deposition in the brain. Here we present four HSD cases with different clinical pictures.

Keywords

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Advanced Biomedical Research
Volume 2014, september
September 2014
Pages 1-5