Supratentorial cortical ependymoma: An unusual presentation of a rare tumor


1 Department of Neurology and Pathology, Isfahan Neurosciences Research Center, Alzahra Hospital, Isfahan, Iran

2 Department of Neurology, Isfahan Neurosciences Research Center, Alzahra Hospital, Isfahan, Iran

3 Department of Neurology, Kashani Hospital, Shahrekord University of Medical Sciences, Shahrekord, Iran

4 Resident of Pathology, Isfahan University of Medical Sciences, Isfahan, Iran


Ependymomas are glial tumors derived from ependymal cells lining the ventricles and the central canal of the spinal cord. Two thirds of ependymomas arise in the infratentorial or intraventricles, whereas one-third are located in supratentorial space. But supratentorial "cortical" ependymomas are very rare. We report a case of a cortical ependymoma in a 17-year-old boy. The patient presented with transient recurrent right weakness and diplopia. This tumor was located in the left parieto-occipital region and he had gross total excision. Microscopy and immunohistochemistry showed grade III differentiation ependymoma.


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